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Protocol Details

Characterization of Dysmorphology in Subjects with Creatine Transporter Deficiency

This study is currently recruiting participants.

Summary | Eligibility | Citations | Contacts

Summary

Number

001074-CH

Sponsoring Institute

National Institute of Child Health and Human Development (NICHD)

Recruitment Detail

Type: Participants currently recruited/enrolled
Gender: Male
Min Age: 2 Years
Max Age: 40 Years

Referral Letter Required

Yes

Population Exclusion(s)

Female

Keywords

Developmental Delay;
Autism Spectrum Disorder;
Children;
Natural History

Recruitment Keyword(s)

None

Condition(s)

Cognitive Disorder;
Metabolic Disease;
Autism Spectrum Disorder

Investigational Drug(s)

None

Investigational Device(s)

None

Intervention(s)

None

Supporting Site

National Institute of Child Health and Human DevelopmentMcMaster University, Ontario, Canada

Background:

Creatine transporter deficiency (CTD) is a genetic disorder that mainly affects the brain in males. CTD causes intellectual disability that can be mild to severe. People with CTD may have seizures and behavioral issues. They may have slow growth and tire easily. CTD may sometimes be confused with autism or other disorders. Better diagnostics are needed. The study team in an NIH study noted that the faces of children with CTD can look similar. For this natural history study, an expert will examine photos of children with CTD. Any shared traits found might help to diagnose CTD.

Objective:

To look for shared facial features of children with CTD.

Eligibility: Males aged 2 to 40 years old with CTD who were in study 17-CH-0020.

Design:

Some participants in study 17-CH-0020 had pictures taken of their faces. The NIH study team wants to share these photos with a colleague in Canada. This person is an expert at evaluating how genetic disorders affect people s bodies.

Participant data collected during the study may also be sent to this expert. This data may include diagnostic images and results from lab tests.

Some children did not have their pictures taken during study 17-CH-0020. Parents are asked to take pictures of these children and send them to the study team. These photos can be sent to a secure portal. The photos can also be taken in-person during a clinic visit.

The photos may be printed in clinical study journals. But this is not required. Parents will be asked to sign a separate consent before the photos are published.

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Eligibility

INCLUSION CRITERIA:

1. Patient is male and between 2-40 years of age, inclusive.

2. Patient has genomic confirmation of a pathologic mutation in the SLC6A8 gene.

3. Patient is able to complete study-related procedures within limitations imposed by condition under study.

4. Patients parents/guardians/caregivers must provide written consent (informed consent) to study-related procedures, and if appropriate, the patient will provide an assent.

EXCLUSION CRITERIA:

1. Patient has had status epilepticus within 3 months of screening.

2. Patients has had a seizure that lasts 5 minutes or longer, and a second seizure without recovering consciousness from the first one, or if a person has repeated seizures for 30 minutes or longer.

3. Patient is unable to comply with the study procedures or has a clinical disease or laboratory abnormality that in the opinion of the investigator would potentially increase the risk of participation.


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Citations:

Not Provided

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Contacts:

Principal Investigator

Referral Contact

For more information:

John R. Perreault, C.R.N.P.
National Institute of Child Health and Human Development (NICHD)
NIHBC 10 - CLINICAL CENTER BG RM 8N248C
10 CENTER DR
BETHESDA MD 20892
(301) 827-9235
john.perreault@nih.gov

John R. Perreault, C.R.N.P.
National Institute of Child Health and Human Development (NICHD)
NIHBC 10 - CLINICAL CENTER BG RM 8N248C
10 CENTER DR
BETHESDA MD 20892
(301) 827-9235
john.perreault@nih.gov

Office of Patient Recruitment
National Institutes of Health Clinical Center (CC)
Building 61, 10 Cloister Court
Bethesda, Maryland 20892
Toll Free: 1-800-411-1222
Local Phone: 301-451-4383
TTY: TTY Users Dial 7-1-1
ccopr@nih.gov

Clinical Trials Number:

NCT05600946

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